Table 1

Characteristics of patients with Lynch syndrome

All patients
(n=137)
Patients with non-endometrioid endometrial cancer
(n=27)
Age, yearsMedian4949
Range28–7531–73
Gene mutation MLH1 40 (29.2%)5 (18.5%)
MSH2 36 (26.3%)8 (29.6%)
MSH6 17 (12.4%)4 (14.8%)
Unknown44 (32.1%)10 (37%)
StageIA69 (50.3%)14 (51.8%)
IB18 (13.1%)4 (14.8%)
II8 (5.8%)3 (11.1%)
III9 (6.6%)5 (18.5%)
IV1 (0.7%)1 (3.7%)
Unknown32 (24.2%)0
GradeG150 (36.5%)0
G230 (21.9%)0
G328 (20.4%)27 (100%)
Unknown29 (21.2%)0
HistotypeEndometrioid110 (80.2%)0
Serous papillary10 (7.3%)10 (37.1%)
Clear cell7 (5.1%)7 (25.9%)
Undifferentiated3 (2.2%)3 (11.1%)
Mixed7 (5.1%)7 (25.9%)
Follow-up, monthsMedian135.3134
Range10–5501–295