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Extranodal Rosai–Dorfman disease as a pelvic mass
  1. B. J.L. Leiva*,
  2. R. M. Bofill*,
  3. B. U. Sevin and
  4. X. J. Geiger
  1. * Visiting Clinician at the Department of Obstetrics, Mayo Clinic, Jacksonville, Florida
  2. Division of Medical and Surgical Gynecology, Mayo Clinic, Jacksonville, Florida
  3. Department of Laboratory Medicine and Pathology, Mayo Clinic, Jacksonville, Florida
  1. Address correspondence and reprint requests to: Bernd-Uwe Sevin, MD, Division of Medical and Surgical Gynecology, Mayo Clinic, 4500 San Pablo Road, Jacksonville, FL 32224, USA. Email: sevin.bernd-uwe{at}


Rosai–Dorfman disease (RDD) is a rare histiocytic disorder of unknown cause. RDD most commonly involves the cervical lymph nodes, but extranodal involvement has been described. We report the case of a patient with extranodal RDD that presented as a retroperitoneal mass obstructing the left ureter. The patient underwent surgical resection of the mass, followed by a 5-month course of vinblastine. There was no evidence of progressive disease 22 months after surgery.

  • chemotherapy
  • pelvic mass
  • Rosai–Dorfman disease
  • surgical resection

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